relapsing polychondritis

Posted By harishkiran elukoti
relapsing polychondritis

CLINICAL HISTORY A 10 year old female child presented with acute onset of noisy breathing that was aggravated during sleep, not accompanied by runny nose or sore throat. Auscultation of the chest did not reveal any added breath sounds. A clinical diagnosis of biphasic stridor was established. Right sided cauliflower ear was identified on physical examination which was attributed to insect bite in childhood. Retrospectively a saddle deformity of the nose was also recognized. Relapsing polychondritis is a rare multisystem disease of unknown aetiology that is characterised by episodic inflammation of cartilaginous structures resulting in tissue destruction. The disease may develop at any age, although most cases are diagnosed between the ages of 40 and 59. The following is a rare presentation of paediatric relapsing polychondritis. Our patient, a 10 year old child, presented with acute onset of biphasic stridor. A contrast enhanced CT scan of the neck was performed for evaluation of the same. Imaging revealed subglottic stenosis due to laryngeal thickening, together with an ossified auricular cartilage and collapse of nasal septal cartilage. Based on this constellation of findings and in conjunction with histopathological evaluation the diagnosis of relapsing polychondritis was confirmed.

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